Page 13 - World Association of Laparoscopic Surgeons - Journal

Lakkanna Suggaiah et al

Fig. 5: HPE-sertoli cell hyperplasia Fig. 6: Laparoscopic gonadectomy

the diagnosis of CAIS was based on gynecological CONCLUSION
examination, laparoscopy and the karyotyping.
AIS should be suspected in cases with primary amenorrhea.
Partial androgen insensitivity syndrome (PAIS) is
Laparoscopic gonadectomy can be performed safely via a
another category of intersex and is characterized by
small caliber laparoscopy after puberty with long-term low
perineoscrotal hypospadiasis, micropenis and bifid scrotum.
dose hormone therapy because of the increased risk of
The testis may also be undescended. The most severe form malignant transformation of the testicles. Attention to
of PAIS presents as isolated clitromegaly. 7
psychological consideration in such patient is important to
Mild androgen insensitivity syndrome (MAIS) as a
maximize long-term success.
category of AIS was realized following investigation for
male factor infertility which suggested defect in the ACKNOWLEDGMENT
androgen action leading to oligospermia with normal level The authors wish to acknowledge Dr Hemalata Ramdoss
of testosterone and increased life span. 7
for providing technical assistance.
Gonadal tissue can be located in the inguinal canal or
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