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CONCLUSION 13. Hauser GA, Schreiner WE. Mayer-Rokitansky-Kuster
syndrome. Rudimentary solid bipartite uterus with solid vagina.
Mayer-Rokitansky-Kuster-Hauser syndrome (MRKHS) is a Schweiz Med Wschr 1961;91:381.
congenital malformation characterized by an absence of vagina 14. Rosenberg HK, Sherman NH, Tarry WF, Duckett JW, Snyder
associated with a variable abnormality of the uterus and the HM. Mayer-Rokitansky-Kuster-Hauser syndrome: US aid to
urinary tract, but functional ovaries. It is not only worthwhile to diagnosis. Radiology 1986;161:815-19.
be alert for urinary tract anomalies in patients with the MRKH 15. Fisher K, Esham RH, Thorneycroft I. Scoliosis associated with
typical Mayer-Rokitansky-Kuster-Hauser syndrome. South
syndrome but also to study the skeletal and auditory systems Med J 2000;93:243-46.
in these patients. Psychological consideration of patients with 16. Heidenreich W. Genital and extragenital abnormalities in Mayer-
uterovaginal agenesis may dictate the need for early Rokitansky-Kuster syndrome. Dtsch Med Wochenschr
vaginoplasty, which hitherto has been delayed until just before 1988;113:1092-96.
marriage. Surgical correction many times requires the creation 17. Strubbe EH, Lemmens JA, Thijn CJ, Willemsen WN, van Toor
BS. Spinal abnormalities and the atypical form of the Mayer-
of a neovaginal canal by the performance of a neovaginoplasty Rokitansky-Kuster-Hauser syndrome. Skeletal Radiol
which can be done by open surgical or laparoscopic assisted 1992;21:459-62.
techniques. The technology of in vitro fertilization and embryo 18. Strubbe EH, Cremers CW, Willemsen WN, Rolland R, Thijn CJ.
transfer, allowing for collection of oocytes from the genetic The Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome
mother, fertilization by the genetic father and placement into a without and with associated features: Two separate entities.
Clin Dysmorphol 1994;3:192-99.
gestational carrier enables a woman without a uterus to have 19. Strubbe EH, Willemsen WN, Lemmens JA, Thijn CJ, Rolland R.
her own genetic children. Mayer-Rokitansky-Kuster-Hauser syndrome: Distinction
between two forms based on excretory, urographic, sonographic,
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